- An unusual subepithelial dystrophy transmitted as an autosomal dominant trait, also called Honeycomb Dystrophy and classified as a variant of Reis-Bucklers'.
- Presents in childhood.
- Clinical features:
- Symptoms: may present with recurrent painful erosions and decreased vision
- Often difficult to differentiate Honeycomb from Reis-Bucklers dystrophy, however in the former; the corneal surface is smooth, corneal sensation is normal
- Typical honeycomb opacity in the corneal subepithelium region develops in the second decade of life
- Superficial corneal debridement
- Photo therapeutic keratectomy maybe required in patient with severe recurrent erosions or reduced visual function.