An unusual subepithelial dystrophy transmitted as an autosomal dominant trait, also called Honeycomb Dystrophy and classified as a variant of Reis-Bucklers'.
Clinical Features
Presents in childhood.
Symptoms: may present with recurrent painful erosions and decreased vision
Signs
Often difficult to differentiate Honeycomb from Reis-Bucklers dystrophy, however in the former; the corneal surface is smooth, corneal sensation is normal
Typical honeycomb opacity in the corneal subepithelium region develops in the second decade of life
Treatment
Superficial corneal debridement
Photo therapeutic keratectomy maybe required in patient with severe recurrent erosions or reduced visual function.