May occur as an isolated finding or as a spectrum of Axenfeld-Rieger's anomaly
Occurs in approximately 15% of normal eyes
Clinical Features
Thickened or hypertrophied Schwalbe's ring that is anteriorly displaced
Visible through a clear cornea as a sharply defined, concentric white line or opacity anterior to the limbus
When associated with Axenfeld-Rieger's anomaly, bilateral involvement with multiple bridging peripheral iris strands and iris stromal hypoplasia are characteristic