Juxtafoveal Telangiectasia

Idiopathic juxtafoveal telangiectasia type 2 demonstrating abnormal foveal reflex with a slight graying of juxtafoveal retina temporally in the right eye and intraretinal hemorrhages in the left eye. Fluorescein angiogram shows leakage from telangiectatic vessels and blockage from the hemorrhages. Telangiectatic vessels are more commonly observed temporal to the fovea. 

  • A condition that is characterized by exudation or diffusion abnormalities from ectatic (dilated and tortuous blood vessels) and incompetent retinal capillaries in the juxtafoveolar region
  • Can be found as a developmental or congenital vascular anomaly or an acquired condition.

Clinical features:

  • Symptoms: decreased vision secondary to serous exudation, macular edema or hard exudates in areas adjacent to the telangiectasis
  • These patients fall into several subgroups. Generally the entity has been subdivided into 3 groups:
    • Group 1: unilateral parafoveal telangiectasis, congenital or acquired
      • Typically occurs in males
      • Yellow, lipid-rich exudation is usually present at the outer margins of the area of telangiectasis forming circinate-type exudate
    • Group 2: Bilateral parafoveal telangiectasis
      • Occurs in either males or females
      • Usually have bilateral retinal thickening
      • Blunted right-angle venules, superficial retinal crystals, intraretinal pigment plaques, and subretinal neovascularization are common findings
    • Group 3: Bilateral perifoveal telangiectasis with retinal capillary obliteration
      • Progressive loss of vision from the obliteration of the perifoveal capillaries
      • Associated with a variety of systemic diseases including polycythemia, hypoglycemia, ulcerative colitis, multiple myeloma and chronic lymphatic leukemia


  • Early laser photocoagulation maybe helpful in restoring and preserving central acuity for group 1
  • Group 2 and 3 typically do not respond to photocoagulation
  • Treatment of neovascularization when it develops in group 2