Vitreous Amyloidosis

Vitreous Amyloidosis
  • Maybe an isolated finding or as a part of systemic amyloidosis.
  • Can be hereditary such as in Familial Amyloidotic Polyneuropathy or nonhereditary.

Clinical Features

  • Symptoms: slowly progressive bilateral or unilateral decreased in visual acuity.
  • Signs:
    • Unilateral or bilateral typical "glass-wool" or "cobweb" appearance of vitreous opacities
    • Hazy view of the fundus

Management

  • Therapeutic vitrectomy in visually significant cases.